Von Hippel-Lindau Disease Overview
What is von Hippel-Lindau disease?
A person with von Hippel-Lindau disease or angiomatosis retinae
has abnormal cells throughout the body that multiply, forming tumors (hemangioblastomas). The cells can become cancerous and spread to other parts of the body. Von Hippel-Lindau tumors are most common in the abdomen, brain and eyes. Von Hippel-Lindau is an inherited disease that increases a person's risk for kidney cancer. About 3 out of every 100,000 people in the US are born with von Hippel-Lindau disease.
What are the symptoms of von Hippel-Lindau disease?
Symptoms of von Hippel-Lindau disease include abdominal pain, back pain, flank pain, blood in the urine, headaches, and vision changes.
How does the doctor treat von Hippel-Lindau disease?
There is no cure for von Hippel-Lindau disease. Treatment for von Hippel-Lindau disease may include surgery to remove tumors in the kidneys, brain, or eyes.
Continue to Von Hippel-Lindau Disease Incidence
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