Stephen J. Schueler, M.D.

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Von Hippel-Lindau Disease Overview

What is von Hippel-Lindau disease?
A person with von Hippel-Lindau disease or angiomatosis retinae
has abnormal cells throughout the body that multiply, forming tumors (hemangioblastomas). The cells can become cancerous and spread to other parts of the body. Von Hippel-Lindau tumors are most common in the abdomen, brain and eyes. Von Hippel-Lindau is an inherited disease that increases a person's risk for kidney cancer. About 3 out of every 100,000 people in the US are born with von Hippel-Lindau disease.

What are the symptoms of von Hippel-Lindau disease?
Symptoms of von Hippel-Lindau disease include abdominal pain, back pain, flank pain, blood in the urine, headaches, and vision changes.

How does the doctor treat von Hippel-Lindau disease?
There is no cure for von Hippel-Lindau disease. Treatment for von Hippel-Lindau disease may include surgery to remove tumors in the kidneys, brain, or eyes.

Continue to Von Hippel-Lindau Disease Incidence

Last Updated: Apr 26, 2011 References
Authors: Stephen J. Schueler, MD; John H. Beckett, MD; D. Scott Gettings, MD
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PubMed Von Hippel-Lindau Disease References
  1. Joerger M, Koeberle D, Neumann HP, Gillessen S. Von Hippel-Lindau disease--a rare disease important to recognize. Onkologie. 2005 Mar;28(3):159-63. [15772467]
  2. Maher ER. Von Hippel-Lindau disease. Curr Mol Med. 2004 Dec;4(8):833-42. [15579030]
  3. Richard S; French VHL Study Group. von Hippel-Lindau disease: recent advances and therapeutic perspectives. Expert Rev Anticancer Ther. 2003 Apr;3(2):215-33. [12722881]
  4. Slater A, Moore NR, Huson SM. The natural history of cerebellar hemangioblastomas in von Hippel-Lindau disease. AJNR Am J Neuroradiol. 2003 Sep;24(8):1570-4. [13679272]
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