Stephen J. Schueler, M.D.

Overview Symptoms

Pulmonary Alveolar Proteinosis Overview

What is pulmonary alveolar proteinosis?
A person with pulmonary alveolar proteinosis has a rare lung disease where a type of protein builds up in the alveoli of the lungs making it difficult to breath. The underlying cause for pulmonary alveolar proteinosis is not clear, although there appears to be two forms of the disease: primary and secondary. Primary disease is idiopathic, which means that it occurs for unknown reasons. Secondary pulmonary alveolar proteinosis develops due to lung infection, cancer, or following the inhalation of mineral dusts or insecticides.

What are the symptoms of pulmonary alveolar proteinosis?
The symptoms of pulmonary alveolar proteinosis include cough, fatigue, fever, unintentional weight loss and shortness of breath.

How does the doctor treat pulmonary alveolar proteinosis?
The treatment of pulmonary alveolar proteinosis includes periodically washing out the protein from the lungs. A lung transplant may be recommended with some that develop this disease.

Continue to Pulmonary Alveolar Proteinosis Symptoms

Last Updated: Jun 7, 2011 References
Authors: Stephen J. Schueler, MD; John H. Beckett, MD; D. Scott Gettings, MD
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PubMed Pulmonary Alveolar Proteinosis References
  1. Juvet SC, Hwang D, Waddell TK, Downey GP. Rare lung disease II: pulmonary alveolar proteinosis. Can Respir J. 2008 May-Jun;15(4):203-10. Review. PubMed [18551202]
  2. Suzuki T, Sakagami T, Rubin BK, Nogee LM, Wood RE, Zimmerman SL, Smolarek T, Dishop MK, Wert SE, Whitsett JA, Grabowski G, Carey BC, Stevens C, van der Loo JC, Trapnell BC. Familial pulmonary alveolar proteinosis caused by mutations in CSF2RA. J Exp Med. 2008 Nov 24;205(12):2703-10. Epub 2008 Oct 27. [18955570]
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