Acute Intermittent Porphyria Treatment
Episodes of acute intermittent porphyria may be prevented by eating a special diet, avoiding alcohol, and avoiding exposure to the sun. Sudden acute intermittent porphyria is treated in the hospital with intravenous heme therapy, which reduces the production of porphyrins. Additional treatment includes a high carbohydrate diet and medication for pain. Porphyria requires life-long treatment.
General treatment for acute intermittent porphyria includes:
- Avoid medications that trigger porphyria.
- Do not take iron supplements.
- Do not drink alcohol.
- Avoid fasting.
- Avoid sun exposure.
- Eat a high carbohydrate diet.
- Take vitamin A supplements.
Treatment for a severe attack of acute intermittent porphyria may include:
Acute Intermittent Porphyria Questions For Doctor
The following are some important questions to ask before and after the treatment of acute intermittent porphyria.
Questions to ask before treatment:
- What are my treatment options?
- Is surgery an option for me?
- What are the risks associated with treatment?
- Do I need to stay in the hospital?
- How long will I be in the hospital?
- What are the complications I should watch for?
- How long will I be on medication?
- What are the potential side effects of my medication?
- Does my medication interact with nonprescription medicines or supplements?
- Should I take my medication with food?
Questions to ask after treatment:
- Do I need to change my diet?
- Do I need to lose weight?
- Are there any medications or supplements I should avoid?
- When can I resume my normal activities?
- When can I return to work?
- What else can I do to reduce my risk for having this problem again?
- How often will I need to see my doctor for checkups?
- What local support and other resources are available?
Acute Intermittent Porphyria Specialist
Continue to Acute Intermittent Porphyria Home Care
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- Sassa S. Diagnosis and therapy of acute intermittent porphyria. Blood Rev. 1996 Mar;10(1):53-8.